The following provides commonly used ICD-10-CM codes for lipid management and prevention.
Dyslipidemia & Inherited Risk
E78.00 – Pure hypercholesterolemia
E78.41 – Elevated lipoprotein(a)
E78.1 – Pure hypertriglyceridemia
E78.5 – Hyperlipidemia, unspecified
E78.2 – Mixed hyperlipidemia
Familial Hypercholesterolemia
E78.010 – Homozygous familial hypercholesterolemia
E78.011 – Heterozygous familial hypercholesterolemia
E78.019 – Familial hypercholesterolemia, unspecified
Lipid Disorders (Other)
E78.6 – Abetalipoproteinemia
E78.41 – Cerebrotendinous xanthomatosis
E78.2– Dysbetalipoproteinemia
E78.5 – Familial chylomicronemia syndrome
E75.6 – LCAT deficiency
E75.5 – Lysosomal acid lipase deficiency
E78.3 – Multifactorial chylomicronemia syndrome
E78.3 – Persistent chylomicronemia syndrome
E78.3 – Severe hypertriglyceridemia
Lipodystrophies
E88.10 – Lipodystrophy, unspecified
E88.11 – Partial lipodystrophy
E88.12 – Generalized lipodystrophy
E88.13 – Localized lipodystrophy
E88.14 – HIV-associated lipodystrophy
E88.19 – Other lipodystrophy NEC
Statin Intolerance/Adverse Event
Z88.8 – Other drug intolerance (primary “statin intolerance” code)
T46.6X5Z – Adverse effect of antihyperlipidemic & antiarteriosclerotic drugs, initial encounter (only if documenting an “adverse effect” event)
Imaging-Defined Coronary Atherosclerosis (CAC/CCTA)
I25.10 – Atherosclerotic heart disease of native coronary artery without angina
I25.84 – Coronary atherosclerosis due to calcified coronary lesion
This information is intended as informational materials for healthcare professionals and practices only.
Updated: July 2026