Infographics

ICD-10 Codes

The following provides commonly used ICD-10-CM codes for lipid management and prevention.

Dyslipidemia & Inherited Risk

E78.00 – Pure hypercholesterolemia

E78.41 – Elevated lipoprotein(a)

E78.1 – Pure hypertriglyceridemia

E78.5 – Hyperlipidemia, unspecified

E78.2 – Mixed hyperlipidemia

Familial Hypercholesterolemia

E78.010 – Homozygous familial hypercholesterolemia

E78.011 – Heterozygous familial hypercholesterolemia

E78.019 – Familial hypercholesterolemia, unspecified

Lipid Disorders (Other)

E78.6 – Abetalipoproteinemia

E78.41 – Cerebrotendinous xanthomatosis

E78.2– Dysbetalipoproteinemia

E78.5 – Familial chylomicronemia syndrome

E75.6 – LCAT deficiency

E75.5 – Lysosomal acid lipase deficiency

E78.3 – Multifactorial chylomicronemia syndrome

E78.3 – Persistent chylomicronemia syndrome

E78.3 – Severe hypertriglyceridemia

Lipodystrophies

E88.10 – Lipodystrophy, unspecified

E88.11 – Partial lipodystrophy

E88.12 – Generalized lipodystrophy

E88.13 – Localized lipodystrophy

E88.14 – HIV-associated lipodystrophy

E88.19 – Other lipodystrophy NEC

Statin Intolerance/Adverse Event

Z88.8 – Other drug intolerance (primary “statin intolerance” code)

T46.6X5Z – Adverse effect of antihyperlipidemic & antiarteriosclerotic drugs, initial encounter (only if documenting an “adverse effect” event)

Imaging-Defined Coronary Atherosclerosis (CAC/CCTA)

I25.10 – Atherosclerotic heart disease of native coronary artery without angina

I25.84 – Coronary atherosclerosis due to calcified coronary lesion

This information is intended as informational materials for healthcare professionals and practices only.

Updated: July 2026